| CPC A61K 31/198 (2013.01) [A61P 25/28 (2018.01)] | 13 Claims |

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1. A method for treating a lysosomal storage disorder (LSD) comprising:
directly delivering leucine, or a pharmaceutically acceptable salt thereof, to the central nervous system of a subject having LSD or one or more symptoms associated with a LSD;
wherein the leucine, or pharmaceutically acceptable salt thereof, is delivered in a therapeutically effective amount to treat the LSD or the one or more symptoms associated with the LSD;
wherein the direct delivery is by an administration chosen from intrathecal administration and intracranial administration;
wherein the LSD is chosen from Tay-Sachs disease, the AB variant of Tay-Sachs disease, Sandhoff disease, Niemann-Pick type A disease, Niemann-Pick type B disease, Niemann-Pick type C disease, Fabry disease, neuronal ceroid lipofuscinoses, Krabbe disease, Farber disease, Gaucher disease, metachromatic leukodystrophy, multiple sulphatase deficiency, mucolipidosis II, mucolipidosis III, MPS III, MPS VII, GM1 gangliosidosis, and aspartylglucosaminuria; and
wherein the leucine is not acetyl-leucine and wherein the therapeutically effective amount of leucine is administered to the subject for a duration chosen from at least about 3 months, at least about 6 months, at least about 1 year, at least about 2 years, and at least about 5 years.
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