| CPC A61K 31/198 (2013.01) [A21D 2/245 (2013.01); A21D 13/80 (2017.01); A23L 33/15 (2016.08); A23L 33/16 (2016.08); A23L 33/175 (2016.08); A61K 9/0053 (2013.01); A61K 9/0056 (2013.01); A61K 9/1635 (2013.01); A61K 9/1652 (2013.01); A61K 9/205 (2013.01); A61K 9/5015 (2013.01); A61K 9/5047 (2013.01); A61K 9/5073 (2013.01); A61K 9/5115 (2013.01); A61K 9/5123 (2013.01); A61K 9/5138 (2013.01); A61K 9/5161 (2013.01); A61K 31/00 (2013.01); A61K 31/401 (2013.01); A61K 31/405 (2013.01); A61K 31/4172 (2013.01); A61K 33/00 (2013.01); A61P 3/00 (2018.01); A23V 2002/00 (2013.01); A61K 2300/00 (2013.01)] | 16 Claims |

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1. A method of treating phenylketonuria comprising orally administering to a subject in need thereof, an effective amount of a modified release amino acid formulation, the formulation comprising a plurality of modified release granules and a plurality of tyrosine-containing granules, the modified release granules comprising:
a) a sodium alginate binder admixed with an amino acid component, the amino acid component comprising at least 15 amino acids selected from the group consisting of L-alanine at 2.0 to 12.0 weight percent, L-arginine at 3.0 to 10.5 weight percent, L-aspartic acid at 5.0 to 10.5 weight percent, L-cystine at 1.5 to 4.0 weight percent, L-glutamine at 7.0 to 25.0 weight percent, glycine at 3.5 to 15.0 weight percent, L-histidine at 2.0 to 6.5 weight percent, L-isoleucine at 2.0 to 8.5 weight percent, L-leucine at 8.0 to 15.0 weight percent, L-lysine at 4.5 to 10.5 weight percent, L-methionine at 1.0 to 3.0 weight percent, L-proline at 3.5 to 15.0 weight percent, L-serine at 2.0 to 8.5 weight percent, L-threonine at 4.0 to 7.5 weight percent, L-tryptophan at 1.0 to 4.0 weight percent, L-valine at 2.5 to 10.0 weight percent, L-carnitine, L-glutamic acid, and taurine; and
b) an ethylcellulose coating layer that coats the modified release granules; and
wherein
no more than 70% of the amino acids in the formulation are released after 30 minutes when the formulation is subjected to dissolution testing in a <711>USP 39 NF 34 paddle apparatus at 37° C. in 500 ml 0.1 N hydrochloric acid at a paddle speed of 50 rpm,
further wherein
the L-Tyrosine is present in the formulation from 2.5-14.0 weight %.
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